Pleuropneumoblastoma, a rare pediatric tumor about a case at Ngaoundéré Regional Hospital-Cameroon

Abstract

Pleuropneumoblastoma (PPB) is a rare and aggressive neoplasm that affects children almost exclusively under the age of 5 or 6 years. About 500 cases have been reported to date. This case report presents a case of 10 years old female who was admitted at Emergency Department of Ngaoundere Regional hospital with fever, non productive cough and dyspnea. Aa chest X-ray was immediately performed and showed a complete opacification of her left hemithorax. Then she underwent a chest CT scan suggested the diagnosis of PPB, which was been confirmed by the histo-pathological examination of a biopsy taken from the tumour. This case contibute to the knowledge of this rare event and when a large hemithorax mass is identified in a young child, pleuropneumoblastoma should be considered as the differential diagnosis.